Comprehensive scores incorporating clinical, lung function, imaging and laboratory data will become essential in the future for predicting disease pr…
Gene modifiers of cystic fibrosis lung disease: A systematic review
The constant-phase model (CPM) is commonly fit to respiratory system input impedance (Z rs) to estimate lung mechanics.
In this cohort, as compared with the AREST CF cohort, the authors highlight the limited correlation between infection and inflammation with lung func…
Early Lung Disease in Infants and Preschool Children with Cystic Fibrosis. What Have We Learned and What
associated with inflammation and structural lung disease in young children with cystic fibrosis
This paper is a review of lung function tests best suited to use for early detection of lung disease in Cystic Fibrosis.
Interstitial lung disease in children comprises a range of different rare diseases
Understanding early triggers of Cystic Fibrosis Lung Disease
Predicting disease progression in cystic fibrosis